Erschienen in:
01.03.2011 | Case Report
Rapid spontaneous regression of multicentric infantile myofibromatosis in the posterior fossa and lumbar vertebra
verfasst von:
Tomoru Miwa, Shizuo Oi, Yuichiro Nonaka, Ryo Tamogami, Hikaru Sasaki, Masaharu Akiyama, Yuki Yuza, Kentaro Yokoi, Yuichi Yokokawa, Hiroyuki Ida
Erschienen in:
Child's Nervous System
|
Ausgabe 3/2011
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Excerpt
Infantile myofibromatosis is the most common fibrous tumor of infancy and early childhood. It typically occurs in skin, subcutaneous tissue, muscle, bone, and/or viscera. In patients without visceral involvement, the prognosis is excellent, generally with spontaneous regression of the tumor nodules in 1 to 2 years [
1]. However, they show unfavorable prognosis within the first few months of life if there is visceral involvement [
1]. Intracranial involvement is rare, and to our knowledge, only 17 such cases have been reported [
1‐
15]. Although lesions usually arise from the dura [
16] and grow in one direction, either epidural or subdural, in our case, there was equal growth epidurally and subdurally. Spontaneous regression occurred at the same time as that of a lumbar lesion 3 months after biopsy. This unique course has never been reported, and the rate of regression in this case was remarkable. …