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Erschienen in: Pediatric Surgery International 10/2009

01.10.2009 | Original Article

Tethered cord in patients with anorectal malformation: preliminary results

verfasst von: A. Suppiej, L. Dal Zotto, A. Cappellari, A. Traverso, M. Castagnetti, P. Drigo, P. Midrio

Erschienen in: Pediatric Surgery International | Ausgabe 10/2009

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Abstract

Background

A tethered cord (TC) has been reported in as much as 50% of the patients affected by anorectal malformation (ARM). No guidelines for timing and modality of diagnosis and treatment have been established. We present the preliminary results of a multidisciplinary protocol carried out at our center.

Methods

Seventy-four ARM patients underwent spinal magnetic resonance imaging (MRI). All TC patients underwent videourodynamic (UD), somatosensory-evoked potentials (SEPs), and neurological examination at baseline and, if normal, at 5 and 10 years of age. Conversely, when UD or SEP abnormalities were detected the follow-up was individually tailored at shorter time.

Results

25/74 patients had a neuroradiological TC (33.7%). Based on the results of UD, SEP, and neurological status, four patients were untethered, eight are possible candidates, nine are stable, and four were excluded because of incomplete data.

Discussion

Tethered cord is frequent in ARM patients. Because neurological deficits secondary to TC can contribute to neurological disability, we recommend routine MRI examination and a multidisciplinary program of follow-up in cases of TC. Preliminary results suggest the combined use of SEPs and UD could represent a useful adjunct to clinical examination in patients in whom a “wait and see” approach is preferred to the prophylactic surgery.
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Metadaten
Titel
Tethered cord in patients with anorectal malformation: preliminary results
verfasst von
A. Suppiej
L. Dal Zotto
A. Cappellari
A. Traverso
M. Castagnetti
P. Drigo
P. Midrio
Publikationsdatum
01.10.2009
Verlag
Springer-Verlag
Erschienen in
Pediatric Surgery International / Ausgabe 10/2009
Print ISSN: 0179-0358
Elektronische ISSN: 1437-9813
DOI
https://doi.org/10.1007/s00383-009-2435-6

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