Erschienen in:
01.03.2008 | Case Report
Papillary tumor of the pineal region in a child: case report and review of the literature
verfasst von:
Kévin Buffenoir, Philippe Rigoard, Michel Wager, Sarah Ferrand, Alix Coulon, Jean Luc Blanc, Benoit Bataille, Antoine Listrat
Erschienen in:
Child's Nervous System
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Ausgabe 3/2008
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Abstract
Case report
A 13-year-old boy presented with a history of intracranial hypertension. Radiologic studies revealed triventricular hydrocephalus secondary to a space-occupying lesion in the pineal region. Endoscopic third ventriculostomy was performed to treat hydrocephalus, and the lesion was biopsied. Complete resection of the tumor was subsequently performed. After a period of uncertainty, the diagnosis of papillary tumor of the pineal region was established. Tumor bed radiotherapy at a dose of 50 Gy was associated. With a follow-up of 15 months, the postoperative course was satisfactory with return to school and no residual tumor on magnetic resonance imaging.
Conclusion
Papillary tumors of the pineal region constitute a rare entity, with a difficult diagnosis, an uncertain prognosis, and a high risk of local recurrence; they must be treated by a combination of surgery and radiotherapy. The only identified prognostic factor is the complete or incomplete nature of surgical resection.