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Erschienen in: Pediatric Nephrology 8/2006

01.08.2006 | Brief Report

Tuberous sclerosis complex and renal angiomyolipoma: case report and review of the literature

verfasst von: Elisabeth B. Winterkorn, Ghaleb H. Daouk, Sudha Anupindi, Elizabeth A. Thiele

Erschienen in: Pediatric Nephrology | Ausgabe 8/2006

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Abstract

A 5-year-old boy with a known diagnosis of tuberous sclerosis complex was found to have an enlarging renal mass on routine ultrasound. He was diagnosed with an angiomyolipoma (AML) and scheduled for close observation. Follow-up magnetic resonance imaging demonstrated the AML to be significantly enlarged and hypervascular. Selective arterial embolization of the tumor was performed, which resulted in an appropriate decrease in tumor size. Angiomyolipoma is a known and well-described complication of the tuberous sclerosis complex that is usually found among patients in their adolescent and adult years. The case presented here illustrates the need for early and repeated renal imaging of younger pediatric patients with tuberous sclerosis. Our experience adds to the literature on young pediatric patients requiring embolization for treatment of large renal angiomyolipomas.
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Metadaten
Titel
Tuberous sclerosis complex and renal angiomyolipoma: case report and review of the literature
verfasst von
Elisabeth B. Winterkorn
Ghaleb H. Daouk
Sudha Anupindi
Elizabeth A. Thiele
Publikationsdatum
01.08.2006
Verlag
Springer Berlin Heidelberg
Erschienen in
Pediatric Nephrology / Ausgabe 8/2006
Print ISSN: 0931-041X
Elektronische ISSN: 1432-198X
DOI
https://doi.org/10.1007/s00467-006-0133-3

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